Search on: HIRSCHSPRUNG DISEASE 
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Descriptor English:   Hirschsprung Disease 
Descriptor Spanish:   enfermedad de Hirschsprung 
Descriptor Portuguese:   Doença de Hirschsprung 
Synonyms English:   Aganglionic Megacolon
Aganglionosis, Colonic
Aganglionosis, Rectosigmoid
Aganglionosis, Rectosigmoid Colon
Aganglionosis, Total Colonic
Colonic Aganglionosis
Congenital Intestinal Aganglionosis
Congenital Megacolon
Disease, Hirschsprung
Disease, Hirschsprung's
Hirschsprung's Disease
Hirschsprungs Disease
Megacolon, Aganglionic
Megacolon, Congenital
Rectosigmoid Aganglionosis
Rectosigmoid Colon Aganglionosis
Total Colonic Aganglionosis  
Tree Number:   C06.198.439
C06.405.469.158.701.439
C16.131.314.439
Definition English:   Congenital MEGACOLON resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the LARGE INTESTINE. The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases, the aganglionic segment is within the RECTUM and SIGMOID COLON. 
Indexing Annotation English:   acquired megacolon = MEGACOLON
History Note English:   83; was HIRSCHSPRUNG'S DISEASE see MEGACOLON 1963-82 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications DI diagnosis
DG diagnostic imaging DH diet therapy
DT drug therapy EC economics
EM embryology EN enzymology
EP epidemiology EH ethnology
ET etiology GE genetics
HI history IM immunology
ME metabolism MI microbiology
MO mortality NU nursing
PS parasitology PA pathology
PP physiopathology PC prevention & control
PX psychology RT radiotherapy
RH rehabilitation SU surgery
TH therapy UR urine
VE veterinary VI virology
Record Number:   6786 
Unique Identifier:   D006627 

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